Clinical features of urticarial vasculitis

	Cutaneous features	Systemic features
Common	Erythematous urticarial papules and plaques (wheals), angioedema, dermographism, annular erythema	Musculoskeletal: arthralgia, arthritis
Less common	Urticarial lesions with residual hyperpigmentation and/or purpura	Respiratory: cough, dyspnea, hemoptysis, COPD, asthma, pleural effusion
		Renal disease: proteinuria, hematuria, glomerulonephritis
		Gastrointestinal: substernal pain, abdominal pain, nausea, vomiting, diarrhea
Rare	Erythema multiforme-like lesions, livedo reticularis, Raynaud's phenomenon, laryngeal edema	Cardiac: pericarditis, pericardial effusion, cardiac tamponade
		Ophthalmologic: conjunctivitis, episcleritis, uveitis, geographic serpiginous choroidopathy, visual loss
		Other: fever, splenomegaly, lymphadenopathy, cold sensitivity, reversible tracheal stenosis
Very rare		CNS: pseudotumor cerebri, cranial nerve palsies, aseptic meningitis
		Miscellaneous: transverse myelitis, cardiac valve disease, optic atrophy, Jaccoud's arthropathy (chronic non-erosive, deforming arthropathy), peripheral neuropathy, pleuritis

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