Characteristics of PHACE syndrome

P	Posterior fossa brain malformations, most commonly the Dandy-Walker variant
H	Hemangiomas, particularly large, segmental facial lesions
A	Arterial anomalies
C	Cardiac anomalies and coarctation of the aorta
E	Eye abnormalities and endocrine abnormalities
S*	Sternal cleft, supraumbilical raphe, or both

* The term "PHACE(S)" is sometimes used in the presence of ventral developmental defects.

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