Major diagnostic features |
1. Sensory nerve amplitudes >80 percent of the lower limit of normal in 2 or more nerves |
2. Needle EMG with short-duration, low-amplitude MUPs with early or normal full recruitment, with or without fibrillation potentials |
3. Absence of a decremental response on repetitive nerve stimulation |
4. Muscle histopathologic findings of myopathy with myosin loss |
Supportive features |
1. Motor amplitudes <80 percent lower limit of normal in 2 or more nerves without conduction block |
2. Elevated serum CK (best assessed in the first week of illness) |
3. Demonstration of muscle inexcitability |
4. Prolonged compound muscle action potential durations (>8 milliseconds for all nerves except >15 milliseconds for the fibular motor response to the tibialis anterior) |
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