Congenital nystagmus | Spasmus nutans | |
Features of nystagmus | ||
Waveform | Often mixed with jerk | Strictly pendular |
Amplitude | Large, always >3° | Small, often <3° |
Amplitude asymmetry | Minimal (<25 percent) | >25 percent |
Frequency | Slow, <7Hz | Fast, >7Hz |
Phase relationship | Conjugate | Dysconjugate |
Duration | Constant | Intermittent |
Other features | ||
Age at onset | <6 months | >6 months |
Associated strabismus/amblyopia | More frequent | |
Head nodding | Larger and more frequent | |
Horizontal OKR | Absent or inverted | Normal |
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