Potential disorder | |
Urine color | |
Black (upon standing/oxidation) | Homogentisic aciduria (alkaptonuria) |
Blue | Tryptophan malabsorption |
Pink | Disorders with hematuria, kidney stone formation |
Port wine (upon standing/oxidation) | Porphyrias |
Yellow-orange | Disorders with increased uric acid |
Urine odor* | |
Acrid, sweaty feet | Glutaric acidemia II |
Cabbage | Tyrosinemia |
Fishy | Trimethlylaminuria, dimethylglycinuria |
Maple syrup, curry | Maple syrup urine disease |
Mousy | Phenylketonuria |
Sweaty feet | Isovaleric acidemia |
Sweet | Beta-ketothiolase deficiency |
Swimming pool | Hawkinsinuria |
Do you want to add Medilib to your home screen?