Congestive |
Cirrhosis |
Heart failure |
Thrombosis of portal, hepatic, or splenic veins |
Malignancy |
Lymphoma, usually indolent variants |
Acute and chronic leukemias |
Polycythemia vera |
Multiple myeloma and its variants |
Essential thrombocythemia |
Primary myelofibrosis |
Primary splenic tumors |
Metastatic solid tumors |
Infection |
Viral – Hepatitis, infectious mononucleosis, cytomegalovirus |
Bacterial – Salmonella, Brucella, tuberculosis |
Parasitic – Malaria, schistosomiasis, toxoplasmosis, leishmaniasis |
Infective endocarditis |
Fungal |
Inflammation |
Sarcoid |
Serum sickness |
Systemic lupus erythematosus |
Rheumatoid arthritis (Felty syndrome) |
Infiltrative, nonmalignant |
Gaucher disease |
Niemann-Pick disease |
Amyloid |
Other lysosomal storage diseases (eg, mucopolysaccharidoses) |
Langerhans cell histiocytosis |
Hemophagocytic lymphohistiocytosis |
Rosai-Dorfman disease |
Hematologic (hypersplenic) states |
Acute and chronic hemolytic anemias, all etiologies |
Sickle cell disease (children) |
Following use of recombinant human granulocyte colony-stimulating factor |
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