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Classification of idiopathic interstitial pneumonias

Classification of idiopathic interstitial pneumonias
Category Clinical-radiologic-pathologic diagnoses Associated radiologic and/or pathologic-morphologic patterns
Chronic fibrosing IP Idiopathic pulmonary fibrosis Usual interstitial pneumonia
Idiopathic nonspecific interstitial pneumonia Nonspecific interstitial pneumonia
Smoking-related IP* Respiratory bronchiolitis-interstitial lung disease Respiratory bronchiolitis
Desquamative interstitial pneumonia Desquamative interstitial pneumonia
Acute/subacute IP Cryptogenic organizing pneumonia Organizing pneumonia
Acute interstitial pneumonia Diffuse alveolar damage

IP: interstitial pneumonia.

* Desquamative interstitial pneumonia can occasionally occur in nonsmokers.
Reprinted with permission of the American Thoracic Society. Copyright © 2020 American Thoracic Society. All rights reserved. From: Travis WD, Costabel U, Hansell DM, et al. An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med 2013; 188:733. The American Journal of Respiratory and Critical Care Medicine is an official journal of the American Thoracic Society.
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