Disorder | Prevalence (%) |
Polyglandular autoimmune syndrome type 1 | |
Endocrine | |
Hypoparathyroidism | 89 |
Chronic mucocutaneous candidiasis | 75 |
Adrenal insufficiency | 60 |
Primary hypogonadism | 45 |
Hypothyroidism | 12 |
Type 1 diabetes mellitus | 1 |
Hypopituitarism | <1 |
Diabetes insipidus | <1 |
Nonendocrine | |
Malabsorption syndromes | 25 |
Alopecia totalis or areata | 20 |
Pernicious anemia | 16 |
Chronic active hepatitis | 9 |
Vitiligo | 4 |
Polyglandular autoimmune syndrome type 2 | |
Endocrine | |
Adrenal insufficiency | 100 |
Autoimmune thyroid disease | 70 |
Type 1 diabetes mellitus | 50 |
Primary hypogonadism | 5 to 50 |
Diabetes insipidus | <1 |
Nonendocrine | |
Vitiligo | 4 |
Alopecia, pernicious anemia, myasthenia gravis, immune thrombocytopenia purpura, Sjögren syndrome, rheumatoid arthritis | ≤1 |
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