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Estimated frequency and type of pericardial involvement in connective tissue diseases, granulomatous diseases, and autoinflammatory diseases

Estimated frequency and type of pericardial involvement in connective tissue diseases, granulomatous diseases, and autoinflammatory diseases
Systemic disease Estimated frequency of pericardial involvement (percent) Type of pericardial involvement
Connective tissue diseases
Systemic lupus erythematosus >50 Pericardial effusion, pericarditis
Rheumatoid arthritis 10 to 30 Pericardial effusion (30%), pericarditis (10%)
Systemic sclerosis Symptomatic (<20), overall (>60) Pericardial effusion, pericarditis
Polymyositis and dermatomyositis <10 Pericarditis, pericardial effusion, cardiac tamponade (case reports)
Mixed connective tissue disease 10 to 30 Pericarditis, pericardial effusion
Sjögren's disease <30 Pericarditis
Behcet disease Rare Pericarditis
Granulomatous diseases
Sarcoidosis Rare Pericardial effusion, pericarditis
Autoinflammatory diseases
Familial Mediterranean Fever (FMF) 1 Pericarditis
TNF receptor-1 associated periodic syndrome (TRAPS) Rare Pericarditis
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