Single joint involvement |
Septic arthritis or osteomyelitis |
Juvenile idiopathic arthritis |
Lyme disease in endemic areas |
Reactive arthritis |
Hemarthrosis due to trauma, vascular malformation, or bleeding diathesis |
Malignancies such as acute lymphoblastic leukemia and malignant tumors |
Benign tumors such as osteoid osteoma, pigmented vilonodular synovitis |
Multiple joint involvement |
Acute rheumatic conditions |
Systemic lupus erythematous |
Juvenile dermatomyositis |
Sarcoidosis |
Sjögren's syndrome |
Mixed connective tissue disease |
IgA vasculitis (Henoch-Schönlein purpura) |
Scleroderma |
Juvenile idiopathic arthritis |
Reactive arthritis |
Lyme disease |
Malignancy |
Immunodeficiency-associated arthritis |
Inflammatory bowel disease-associated arthritis |
Other |
Chronic recurrent multifocal osteomyelitis |
Chronic infantile neurologic cutaneous and arthritis syndrome (CINCA), also known as neonatal-onset multisystem inflammatory disease (NOMID) |
Prominent systemic features and joint pain |
Acute rheumatic conditions |
Systemic lupus erythematous |
Mixed connective tissue disease |
Kawasaki disease |
IgA vasculitis (Henoch-Schönlein purpura) |
Juvenile dermatomyositis |
Systemic juvenile idiopathic arthritis |
Macrophage activation syndrome |
Systemic vasculitis |
Malignancy such as neuroblastoma, leukemia |
Acute rheumatic fever |
Bacterial infection (tuberculosis, gonococcal infection, Lyme disease, and Brucella infection) |
Viral infection (Epstein-Barr, parovirus, and hepatitis B) |
Parasitic infection (malaria) |
Inflammatory bowel disease-associated arthritis |
Autoinflammatory disorders |
Periodic fever syndromes |
Chronic infantile neurologic cutaneous and arthritis syndrome (CINCA), also known as neonatal-onset multisystem inflammatory disease (NOMID) |
Cryopyrin-associated periodic syndromes (CAPS) |
Pain without joint swelling |
Hip disease |
Legg-Calvé-Perthes disease |
Slipped upper femoral epiphysis (slipped capital femoral epiphysis) |
Benign hypermobility syndrome |
Inherited metabolic disorders |
Gaucher disease |
Sheie disease |
Osteochondroses |
Osgood-Schlatter disease |
Scheuermann disease |
Idiopathic pain syndromes |
Growing pains |
Complex regional pain syndrome |
Fibromyalgia |
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