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Plastic embedded renal tissue demonstrating glycolipid inclusion bodies in distal tubules, with relative sparing of proximal tubules, and interstitial fibrosis (toluidine blue stain, original magnification X80)

Plastic embedded renal tissue demonstrating glycolipid inclusion bodies in distal tubules, with relative sparing of proximal tubules, and interstitial fibrosis (toluidine blue stain, original magnification X80)
Reproduced with permission from: Branton MH, Schiffmann R, Sabnis SG, et al. Natural history of Fabry renal disease: influence of alpha-galactosidase A activity and genetic mutations on clinical course. Medicine 2002; 81:122. Copyright © 2002 Lippincott Williams & Wilkins.
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