INSS Stage | Age | MYCN Status | Pathology Classification | DNA Ploidy | Risk Group Assignment |
1 | 0-21y | Any | Any | Any | Low |
2 | <365 d | Any | Any | - | Low |
>365d-21y | Non-Amp | Any | - | Low | |
>365d-21y | Amp | Favorable | - | Low | |
>365d-21y | Amp | Unfavorable | - | High | |
3 | <365 d | Non-Amp | Any | Any | Intermediate |
<365 d | Amp | Any | Any | High | |
>365d-21y | Non-Amp | Favorable | - | Intermediate | |
>365d-21y | Non-Amp | Unfavorable | - | High | |
>365d-21y | Amp | Any | - | High | |
4 | <365 d | Non-Amp | Any | Any | Intermediate |
<365 d | Amp | Any | Any | High | |
>365d-21y | Any | Any | _ | High | |
4S | <365 d | Non-Amp | Favorable | > 1 | Low |
<365 d | Non-Amp | Any | = 1 | Intermediate | |
<365 d | Non-Amp | Unfavorable | Any | Intermediate | |
<365 d | Amp | Any | Any | High |
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