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Disorders and medications associated with idiopathic noncirrhotic portal hypertension

Disorders and medications associated with idiopathic noncirrhotic portal hypertension
Hematologic/neoplastic Medications
  • Liver cancers
  • Sacrococcygeal teratoma
  • Essential thrombocytosis
  • Polycythemia vera
  • Myeloproliferative disorders
  • Lymphoproliferative disorders
  • Multiple myeloma
  • Spherocytosis
  • Sickle cell disease
  • Protein S deficiency
  • Factor V Leiden mutation
  • Hyperhomocysteinemia
  • Antiphospholipid syndrome
  • Metastatic cancer
  • Azathioprine
  • Thioguanine
  • Cyclophosphamide
  • Chlorambucil
  • Busulfan
  • Doxorubicin
  • Cytosine
  • Arabinoside
  • Bleomycin
  • Carmustine
  • Trastuzumab
  • Interleukin-2
  • Oxaliplatin
Immune Miscellaneous
  • Primary biliary cholangitis
  • Polymyositis
  • Sjögren's syndrome
  • Scleroderma
  • CREST syndrome
  • Still's syndrome
  • Polyarteritis nodosa
  • Rheumatoid arthritis
  • Polymyalgia rheumatica
  • Systemic lupus erythematosus
  • Behçet's syndrome
  • Cryoglobulinemia
  • Idiopathic hypereosinophilic syndrome
  • Idiopathic thrombocytopenic purpura
  • Celiac disease
  • Myasthenia gravis
  • HIV infection
  • Common variable immunodeficiency
  • Liver transplantation
  • Renal transplantation
  • Atrial septal defect
  • Ventricular septal defect
  • Pulmonary vein anomalies
  • Congenital portal venous anomalies
  • VATER syndrome
  • Hereditary hemorrhagic telangiectasia
  • Cystinosis
  • Turner's syndrome
CREST: calcinosis cutis, Raynaud phenomenon, esophageal dysmotility, sclerodactyly, telangiectasia; HIV: human immunodeficiency virus; VATER: Vertebral anomalies, anal atresia, TE fistula (tracheoesophageal fistula), renal defects.
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