CHD anatomy* |
I: Simple |
Native disease |
Isolated small ASD |
Isolated small VSD |
Mild isolated pulmonic stenosis |
Repaired conditions |
Previously ligated or occluded ductus arteriosus |
Repaired secundum ASD or sinus venosus defect without significant residual shunt or chamber enlargement |
Repaired VSD without significant residual shunt or chamber enlargement |
II: Moderate complexity |
Repaired or unrepaired conditions |
Aorto-left ventricular fistula |
Anomalous pulmonary venous connection, partial or total |
Anomalous coronary artery arising from the pulmonary artery |
Anomalous aortic origin of a coronary artery from the opposite sinus |
AVSD (partial or complete, including primum ASD) |
Congenital aortic valve disease |
Congenital mitral valve disease |
Coarctation of the aorta |
Ebstein anomaly (disease spectrum includes mild, moderate, and severe variations) |
Infundibular right ventricular outflow obstruction |
Ostium primum ASD |
Moderate and large unrepaired secundum ASD |
Moderate and large persistently patent ductus arteriosus |
Pulmonary valve regurgitation (moderate or greater) |
Pulmonary valve stenosis (moderate or greater) |
Peripheral pulmonary stenosis |
Sinus of Valsalva fistula/aneurysm |
Sinus venosus defect |
Subvalvar aortic stenosis (excluding HCM; HCM not addressed in these guidelines) |
Supravalvar aortic stenosis |
Straddling atrioventricular valve |
Repaired tetralogy of Fallot |
VSD with associated abnormality and/or moderate or greater shunt |
III: Great complexity (or complex) |
Cyanotic congenital heart defect (unrepaired or palliated, all forms) |
Double-outlet ventricle |
Fontan procedure |
Interrupted aortic arch |
Mitral atresia |
Single ventricle (including double inlet left ventricle, tricuspid atresia, hypoplastic left heart, any other anatomic abnormality with a functionally single ventricle) |