Primary systemic vasculitides |
Predominantly small vessel vasculitis |
- Microscopic polyangiitis*
- Churg-Strauss syndrome*
- Granulomatosis with polyangiitis*
- Essential mixed cryoglobulinemia (non-HCV)
- Henoch-Schönlein purpura
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Predominantly medium vessel vasculitis |
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Predominantly large vessel vasculitis |
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Secondary systemic vasculitides associated with one of the following |
Connective tissue diseases |
- Rheumatoid arthritis
- Systemic lupus erythematosus
- Sjögren's syndrome
- Systemic sclerosis
- Dermatomyositis
- Mixed connective tissue disease
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Sarcoidosis |
Behçet syndrome |
Infection (such as HBV, HCV, HIV, CMV, leprosy, Lyme disease, HTLV-I) |
Drugs |
Malignancy |
Inflammatory bowel disease |
Hypocomplementemic urticarial vasculitis syndrome |
Nonsystemic/localized vasculitis |
Nonsystemic vasculitic neuropathy (includes nondiabetic radiculoplexus neuropathy and some cases of Wartenberg's migrant sensory neuritis) |
Diabetic radiculoplexus neuropathy |
Localized cutaneous/neuropathic vasculitis |
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