Classification | Approximate relative frequency (%) | Ectopic urethral location | Penile curvature* | Foreskin appearance | Management |
Forme fruste of hypospadias (incomplete or partial presence of hypospadias) | 10 | Normal location with a urethral pit or ectopic urethra on the distal glans | Normal | Normal to mild asymmetric ventral deficiency (incomplete closure around the glans) |
|
Standard hypospadias with normal glans width (maximal diameter ≥14 mm) | 40 | Distal urethral location on glans or coronal margin | Normal to mild | Ventral deficiency with a dorsal hooded appearance |
|
25 | Proximal urethral location on penile shaft, at the penoscrotal junction, or within the scrotum | Moderate | Ventral deficiency with a dorsal hooded appearance |
| |
Severe with an abnormally small glans (maximal diameter <14 mm) | 20 | Scrotum or perineum with an abnormally small glans (maximal diameter <14 mm) | Severe | Ventral penile foreskin tethering (referred to as short urethral plate) or fusion of the foreskin to the scrotum |
|
Other variants | 5 | ||||
Chordee without hypospadias | Normal urethral opening and glans | Mild to severe | Normal |
| |
Megameatus intact prepuce | Large urethral opening at the coronal margin | Normal | Normal |
|
* Penile curvature is assessed when the penis is erect and classified as normal (0 to 15°), mild (15 to 40°), moderate (40 to 80°), and severe (>80°).
¶ For details on the evaluation of infants with atypical genital appearances or a difference (disorder) of sex development, refer to related UpToDate content.Do you want to add Medilib to your home screen?