One-year access to more than 500 world journals available in the system
-
http://medilib.ir
- Duration of Time : 365 Day
Price : 300$- Special Price : 100$
Transition and management of Ukrainian war refugee children on kidney replacement therapy
Michal Maternik, Roman Andrunevych, Dorota Drożdż, Piotr Czauderna, Ryszard Grenda & Marcin TkaczykÂ
Management of pediatric dialysis and kidney transplant patients after natural or man-made disasters
Lale Sever, Gülseren Pehlivan, Nur Canpolat, Seha Saygılı, AyÅŸe AÄŸbaÅŸ, Ebru Demirgan, Jun Oh, Elena Levtchenko, Dymtro D. Ivanov & Rukshana ShroffÂ
doi : 10.1007/s00467-022-05734-8
Pediatric patients on kidney replacement therapy (KRT) are among the most vulnerable during large-scale disasters, either natural or man-made. Hemodialysis (HD) treatments may be impossible because of structural damage and/or shortage of medical supplies, clean water, electricity, and healthcare professionals.
The potential of RNA-based therapy for kidney diseases
Tjessa Bondue, Lambertus van den Heuvel, Elena Levtchenko & Roland BrockÂ
doi : 10.1007/s00467-021-05352-w
Inherited kidney diseases (IKDs) are a large group of disorders affecting different nephron segments, many of which progress towards kidney failure due to the absence of curative therapies.
An ethical analysis of obesity as a contraindication of pediatric kidney transplant candidacy
Emily R. Berkman, Kelsey L. Richardson, Jonna D. Clark, André A. S. Dick, Mithya Lewis-Newby, Douglas S. Diekema & Aaron G. WightmanÂ
doi : 10.1007/s00467-022-05572-8
The inclusion of body mass index (BMI) as a criterion for determining kidney transplant candidacy in children raises clinical and ethical challenges. Childhood obesity is on the rise and common among children with kidney failure.
Acute kidney injury following multisystem inflammatory syndrome associated with SARS-CoV-2 infection in children: a systematic review and meta-analysis
Anchal Kumar Tripathi, Rakesh Kumar Pilania, Girish Chandra Bhatt, Mahendra Atlani, Amber Kumar & Shikha MalikÂ
doi : 10.1007/s00467-022-05701-3
Multisystem inflammatory syndrome (MIS-C) is a rare paediatric hyper-inflammatory disorder that occurs following SARS-CoV-2 infection. Acute kidney injury (AKI) occurs in approximately one-quarter to one-third of the patients with MIS-C and is associated with poor prognosis in critically ill children. This systematic review is aimed to evaluate the incidence of AKI, mortality, and the need for kidney replacement therapy (KRT) in patients with MIS-C.
An update on lipid apheresis for familial hypercholesterolemia
Christina Taylan & Lutz T. WeberÂ
doi : 10.1007/s00467-022-05541-1
Familial hypercholesterolemia (FH) is an inherited metabolic defect leading to increased total cholesterol and low-density cholesterol (LDL) from birth onwards.
Transition of young adult kidney transplant recipients
Mina Matsuda-Abedini, Stephen D. Marks & Bethany J. FosterÂ
doi : 10.1007/s00467-022-05582-6
Survival of pediatric kidney transplant recipients has improved over the past six decades. However, adolescents and young adults still have the highest graft failure rates of any age group.
A 5-year-old girl with kidney impairment and severe anemia: Questions
Benjamin Steinman, Marcela Del Rio, Anna Zolotnitskaya & Nicole HaydeÂ
A 5-year-old girl with kidney impairment and severe anemia: Answers
Benjamin Steinman, Marcela Del Rio, Anna Zolotnitskaya & Nicole HaydeÂ
A toxic ingestion with an elevated osmolal gap: Questions
Taryn Shea, Angelina Magreni Dixon, George Sam Wang, Gina DeMasellis & Eliza BlanchetteÂ
A toxic ingestion with an elevated osmolal gap: Answers
Angelina Dixon, Taryn Shea, George Sam Wang, Gina DeMasellis & Eliza BlanchetteÂ
ePHex: a phase 3, double-blind, placebo-controlled, randomized study to evaluate long-term efficacy and safety of Oxalobacter formigenes in patients with primary hyperoxaluria
Gema Ariceta, Laure Collard, Saoussen Abroug, Shabbir H. Moochhala, Edward Gould, Abir Boussetta, Mohamed Ben Hmida, Sudarsana De, Tracy E. Hunley, Faical Jarraya, Gloria Fraga, Ana Banos, Elisabeth Lindner, Bastian Dehmel & Gesa SchalkÂ
doi : 10.1007/s00467-022-05591-5
Primary hyperoxalurias (PHs) are rare genetic diseases that increase the endogenous level of oxalate, a waste metabolite excreted predominantly by the kidneys and also the gut.
Precise clinicopathologic findings for application of genetic testing in pediatric kidney transplant recipients with focal segmental glomerulosclerosis/steroid-resistant nephrotic syndrome
Kenichiro Miura, Naoto Kaneko, Taeko Hashimoto, Kiyonobu Ishizuka, Yoko Shirai, Masataka Hisano, Hiroko Chikamoto, Yuko Akioka, Shoichiro Kanda, Yutaka Harita, Toshiyuki Yamamoto & Motoshi HattoriÂ
doi : 10.1007/s00467-022-05604-3
Establishing a molecular genetic diagnosis of focal segmental glomerulosclerosis (FSGS)/steroid-resistant nephrotic syndrome (SRNS) can be useful for predicting post-transplant recurrence.
Clinical relevance of glomerular C4d deposition in children with early IgA nephropathy or Henoch-Schönlein purpura nephropathy
Dan Wu, Lei Lei, Hejia Zhang, Xingfeng Yao, Zhi Chen, Nan Zhang, Jie Ni, Chen Ling, Xiaorong Liu & Xiangmei ChenÂ
doi : 10.1007/s00467-022-05585-3
Both IgA nephropathy (IgAN) and Henoch-Schönlein purpura nephropathy (HSPN) are characterized by glomerular mesangial IgA deposition. Several large studies on adults have suggested that glomerular C4d deposition has prognostic value in IgAN. However, there are few relevant studies on the clinical value of C4d deposition in children with IgAN or HSPN.
Focal segmental glomerulosclerosis and proteinuria associated with Myo1E mutations: novel variants and histological phenotype analysis
Mira Krendel, Sabine Leh, Michael E. Garone, Alcia Edwards-Richards, Jen-Jar Lin, Damien Brackman, Per Knappskog & Alexei MikhailovÂ
doi : 10.1007/s00467-022-05634-x
Pathogenic mutations in the non-muscle single-headed myosin, myosin 1E (Myo1e), are a rare cause of pediatric focal segmental glomerulosclerosis (FSGS). These mutations are biallelic, to date only reported as homozygous variants in consanguineous families.
The association between hypogammaglobulinemia severity and infection risk in rituximab-treated patients with childhood-onset idiopathic nephrotic syndrome
Yuta Inoki, Kentaro Nishi, Mai Sato, Masao Ogura & Koichi KameiÂ
doi : 10.1007/s00467-022-05652-9
Hypogammaglobulinemia is a major adverse effect from rituximab. However, the association between rituximab-induced hypogammaglobulinemia and infection frequency is unknown.
Predictors of kidney complications and analysis of hypertension in children with allogeneic hematopoietic stem cell transplantation
Anar Gurbanov, Bora Gülhan, Barış KuÅŸkonmaz, Fatma Visal Okur, Fatih Ozaltin, Ali Düzova, Duygu Uçkan Çetinkaya & Rezan TopalogluÂ
doi : 10.1007/s00467-022-05599-x
This study aimed to determine incidence of kidney complications in pediatric allogeneic hematopoietic stem cell transplantation (HSCT) patients.
Evaluation of the Claria sharesource system from the perspectives of patient/caregiver, physician, and nurse in children undergoing automated peritoneal dialysis
Bahriye Uzun Kenan1 · Beltinge Demircioglu Kilic2 · Mehtap Akbalık Kara 3 · Aysel Taktak 4 · Aysun Karabay Bayazit 5 · Zeynep Nagehan Yuruk Yildirim6 · Ali Delibas7 · Mehmet Baha Aytac 8 · Secil Conkar9 · Gulsah Kaya Aksoy 10 · Osman Donmez11 · Sibel Yel 12 · Seha Saygili 13 · Okan Akaci14 · Bahar Buyukkaragoz1 · Harika Alpay15 · Sevcan A. Bakkaloglu
doi : 10.1007/s00467-022-05563-9
Automated peritoneal dialysis (APD) is increasingly preferred worldwide. By using a software application (Homechoice with Claria sharesource system (CSS)) with a mod-M added to the APD device, details of the home dialysis treatment become visible for PD nurses and physicians, allowing for close supervision. We aimed to evaluate the perceptions of patients/caregivers, PD nurses, and physicians about the advantages and disadvantages of CSS.
Urine alpha 1-microglobulin-to-creatinine ratio and beta 2-microglobulin-to-creatinine ratio for detecting CAKUT with kidney dysfunction in children
Riku Hamada, Kaori Kikunaga, Tetsuji Kaneko, Shojiro Okamoto, Masako Tomotsune, Osamu Uemura, Koichi Kamei, Naohiro Wada, Takeshi Matsuyama, Kenji Ishikura, Akira Oka & Masataka HondaÂ
doi : 10.1007/s00467-022-05577-3
The leading cause of advanced chronic kidney disease (CKD) in children is congenital anomalies of the kidney and urinary tract (CAKUT). However, the most appropriate parameters of biochemical urine analysis for detecting CAKUT with kidney dysfunction are not known.
Longitudinal changes in uric acid concentration and their relationship with chronic kidney disease progression in children and adolescents
George J. Schwartz, Jennifer L. Roem, Stephen R. Hooper, Susan L. Furth, Donald J. Weaver Jr., Bradley A. Warady & Michael F. SchneiderÂ
doi : 10.1007/s00467-022-05620-3
Elevated serum uric acid concentration is a risk factor for CKD progression. Its change over time and association with CKD etiology and concomitant changes in estimated glomerular filtration rate (eGFR) in children and adolescents are unknown.
Effects of pediatric chronic kidney disease and its etiology on tissue sodium concentration: a pilot study
Fabio R. Salerno, Alireza Akbari, Sandrine Lemoine, Timothy J. Scholl, Christopher W. McIntyre & Guido FillerÂ
doi : 10.1007/s00467-022-05600-7
Sodium-23 magnetic resonance imaging (23Na MRI) allows non-invasive assessment of tissue sodium concentration ([Na+]).
Good outcomes for arteriovenous fistula with buttonhole cannulation for chronic hemodialysis in children and adolescents
Brittany Garza, Jessica Geer, Sarah J. Swartz, Poyyapakkam Srivaths, Tam T. T. Huynh & Eileen D. BrewerÂ
doi : 10.1007/s00467-022-05580-8
Arteriovenous fistula (AVF) is the preferred access for chronic hemodialysis (HD) in children and adolescents, but central venous catheter use is still high.
Differences in health-related quality of life in children with chronic kidney disease as reported by children and parent proxies
You-Lin Tain, Pei-Chen Lu, Hsiao-Ching Kuo & Chien-Ning HsuÂ
doi : 10.1007/s00467-022-05621-2
Correlation between reports of children and parent for health-related quality of life (HRQOL) is not well studied. This study aims to assess the degree of agreement between child self- and parent proxy-rated HRQOL and to identify factors associated with discordance at baseline and during follow-up in Taiwanese children with chronic kidney disease (CKD).
Successful ABO and HLA incompatible kidney transplantation in children in the UK
Eun Yee Hew, Nicos Kessaris, Jelena Stojanovic, Helen Jones, Martin Christian, Anusha Edwards, David V. Milford, Milos Ognjanovic, Mohan Shenoy, Richard J. Baker & Stephen D. MarksÂ
doi : 10.1007/s00467-022-05583-5
There is increasing evidence of good short-term and medium-term outcomes of ABO incompatible (ABOi) and HLA incompatible (HLAi) kidney transplantation with pre-transplant positive crossmatches in paediatric practice.
COVID-19 in pediatric kidney transplantation: a follow-up report of the Improving Renal Outcomes Collaborative
Charles Varnell Jr., Lyndsay A. Harshman, Chunyan Liu, Laurie Smith, Samhar Al-Akash, Gina-Marie Barletta, Paul Brakeman, Abanti Chaudhuri, Paul Fadakar, Lauren Galea, Rouba Garro, Caroline Gluck, David B. Kershaw, Debora Matossian, Hiren P. Patel, Caitlin Peterson, Cozumel Pruette, Saritha Ranabothu, Nancy Rodig, Pamela Singer, Judith Sebestyen VanSickle, Patricia L. Weng, Lara Danziger-Isakov, Michael E. Seifert & David K. HooperÂ
doi : 10.1007/s00467-022-05570-w
We report follow-up data from an ongoing prospective cohort study of COVID-19 in pediatric kidney transplantation through the Improving Renal Outcomes Collaborative (IROC).
Normal saline, the known but least-examined fluid therapy method for preventing heme-induced nephropathy in children with glucose 6 phosphate dehydrogenase deficiency: a randomized controlled clinical trial
Afshin Safaei-Asl, Saba Emami, Adel Baghersalimi, Bahram Darbandi, Afagh Hassanzadeh Rad & Hamidreza BadeliÂ
doi : 10.1007/s00467-022-05594-2
Glucose 6 phosphate dehydrogenase deficiency (G6PDd) is the most common enzyme deficiency in humans.
A quality initiative to improve recognition of fluid overload among pediatric ICU patients requiring continuous kidney replacement therapy: preliminary results
Delphine R. Nelson, Mahima Keswani, Laura Finn, Kalyn Mahoney, Lisa Genualdi & Mathew F. BarhightÂ
doi : 10.1007/s00467-022-05584-4
Initiation of continuous kidney replacement therapy (CKRT) greater than 20% fluid overload is associated with increased morbidity and mortality. We aimed to reduce the number of patients initiated on CKRT greater than 20% fluid overload by 50% in one year by implementation of a quality improvement initiative.
Long-term kidney outcomes in children following continuous kidney replacement therapy
Jeanne Frisby-Zedan, Matthew F. Barhight, Mahima Keswani, Jennifer Arzu & Delphine NelsonÂ
doi : 10.1007/s00467-022-05579-1
Continuous kidney replacement therapy (CKRT) is a mainstay of therapy for management of severe acute kidney injury (AKI) in critically ill pediatric patients. There is limited data on the risk of chronic kidney disease (CKD) after discharge in this population.
Risk factors, outcomes, and predictors of resolution of acute kidney injury in children with diabetic ketoacidosis
Reem Al Khalifah, Ayman Al-Eyadhy, Najd Musibeeh, Anfal Alshalawi, Noor Alanazi, Ayman Alhboob, Gamal Hassan, Mohamad-Hani Temsah, Ali A. N. Alhaboob, Rupesh Raina & Khalid AlhasanÂ
doi : 10.1007/s00467-022-05578-2
Acute kidney injury (AKI) is a common complication in patients with diabetic ketoacidosis (DKA) (incidence 35–77%). AKI evolution during DKA treatment/recovery is poorly understood. Our aim was to assess children with DKA for prevalence, short-term kidney outcomes, severity, and predictors of AKI development and resolution.
Survival of neonates born with kidney failure during the initial hospitalization
Donna J. Claes, Troy Richardson, Matthew W. Harer, Mahima Keswani, Alicia Neu, Allison C. Redpath Mahon, Michael J. Somers, Avram Z. Traum & Bradley A. WaradyÂ
doi : 10.1007/s00467-022-05626-x
Survival to hospital discharge in neonates born with kidney failure has not been previously described.
Cisplatin-induced nephrotoxicity in childhood cancer: comparison between two countries
Zulfan Zazuli, Catharina J. P. Op ’t Hoog, Susanne J. H. Vijverberg, Rosalinde Masereeuw, Shahrad Rod Rassekh, Mara Medeiros, Rodolfo Rivas-Ruiz, Anke H. Maitland-van der Zee & Bruce C. CarletonÂ
doi : 10.1007/s00467-022-05632-z
Various definitions used to describe cisplatin nephrotoxicity potentially lead to differences in determination of risk factors. This study evaluated incidence of kidney injury according to commonly used and alternative definitions in two cohorts of children who received cisplatin.
Lethal neonatal respiratory failure due to biallelic variants in BBS1 and monoallelic variant in TTC21B
Luke Viehl, Daniel J. Wegner, Stanley P. Hmiel, Frances V. White, Sanjay Jain, F. S. Cole & Jennifer A. WambachÂ
doi : 10.1007/s00467-022-05616-z
Bardet-Biedl syndrome (BBS) is a rare, autosomal recessive ciliopathy characterized by early onset retinal dystrophy, renal anomalies, postaxial polydactyly, and cognitive impairment with considerable phenotypic heterogeneity.
Antibody response to 2- and 3-dose SARS-CoV-2 mRNA vaccination in pediatric and adolescent kidney transplant recipients
Clarkson Crane, Erin Phebus & Elizabeth IngulliÂ
doi : 10.1007/s00467-022-05661-8
Additional “booster� doses of mRNA SARS-CoV-2 vaccines have become standard of care for immunosuppressed patients, including kidney transplant recipients (KTR). While these additional doses have been shown to be efficacious in the adult KTR population, there is paucity of data for pediatric and adolescent KTR.
Long-term prognosis of rituximab-induced hypogammaglobulinemia in children with complicated steroid-dependent nephrotic syndrome: impact of multiple rituximab courses
Yuta Onuki & Shuichiro FujinagaÂ
Obituary of Andreas Fanconi, 12 August 1928–5 October 2022
Ernst Leumann & Thomas Jacob NeuhausÂ
